X-Nico

unusual facts about corneal dystrophy



Fasciclin domain

Human TGF-beta induced Ig-H3 (BIgH3) protein (4 FAS1 domains), where the FAS1 domains mediate cell adhesion through an interaction with alpha3/beta1 integrin; mutation in the FAS1 domains result in corneal dystrophy.


see also

Granular corneal dystrophy

Granular corneal dystrophy is caused by a mutation in the TGFBI gene, located on chromosome 5q31.

The name Avellino corneal dystrophy comes from the first four patients in the original study each tracing their family origin to the Italian province of Avellino.